Thoracic Ectopic Cordis in a Nigerian Child
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چکیده
Ectopia cordis is derived from two Latin words which means outside and heart [1]. It is a rare congenital malformation in which the heart is formed outside the thoracic cavity. It occurs in 1 in 5-7 per 1,000,000 live births [2]. It may occur as an isolated defect or in association with other body wall defects that affect the thorax, abdomen or both [3]. It may also be associated with other intra cardiac lesions [4]. Despite advances in cardiac surgery, ectopia cordis is extremely challenging with a few long term survivors even in the most advanced settings [4].
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Extrathoracic heart in northern Cameroon: a case report
Sternal clefts, ectopia cordis, and Cantrell's pentalogy continue to be very rare congenital anomalies in pediatric surgery. The prenatal diagnosis is easily made with ultrasound by visualizing the heart outside the thoracic cavity. Ectopia cordis is frequently associated with other congenital defects involving multiple organ systems. We report a case of ectopia cordis with successful surgical ...
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